
Center for Advanced Practice
Title
Protein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog.
Publication Title
World J Pediatr Congenit Heart Surg
Document Type
Article
PubMed ID
31835975
Abstract
Fontan-associated protein losing enteropathy is a challenge to treat and is a major contributor to morbidity and mortality in patients with palliated single ventricle. Numerous strategies for management have been proposed, with confusion as to how best to stratify and implement care among the many treatments available. Medical management can be helpful in some, while novel lymphatic interventions hold potential for remission with good results. We review our institutional approach to protein losing enteropathy after Fontan operation and provide a suggested algorithm and pathway for effective care.
Keywords
Algorithms, Fontan Procedure, Heart Defects, Congenital, Humans, Postoperative Complications, Protein-Losing Enteropathies
DOI
10.1177/2150135119890555
Publication Date
1-1-2020
Citation
Rychik, J., Dodds, K., Goldberg, D., Glatz, A., Fogel, M., Rossano, J., Chen, J., Pinto, E., Ravishankar, C., Rand, E., Rome, J., & Dori, Y. (2020). Protein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog.. World J Pediatr Congenit Heart Surg, 11 (1), 92-96. https://doi.org/10.1177/2150135119890555